Dentinogenesis Imperfecta Types, Symptoms, Causes, Treatment

Dentinogenesis imperfecta Types, Symptoms, Causes, Treatment

This uncommon defect of collagen formation is transmitted as an autosomal dominant trait. The gene is closely related to that of osteogenesis imperfecta particularly type IV. In types III and IV Osteogenesis Imperfecta, Dentinogenesis Imperfecta is present in over 80% in the primary dentition.

What are the Dentinogenesis Imperfecta Types?

Dentinogenesis Imperfecta Type - 1

Associated with osteogenesis imperfecta.
Deciduous teeth mainly involve.

Dentinogenesis Imperfecta Radiological Features (Type 1): Obliteration of the pulp chamber and reduce radiolucency of the root canal.

Dentinogenesis Imperfecta Type -2

Not associated with osteogenesis imperfect.
Both deciduous and permanent dentition equally involve.

Radiological features: Same as Type 1

Dentinogenesis Imperfecta Type -3

An unusual form of the disease.
Commonly show multiple pulp exposure and periapical lesion.
Both deciduous and permanent dentition are affected.

Radiological features: Pulp chamber and root canal are extremely large. The main feature of all types is short stunned root.

What are the Dentinogenesis Imperfecta Causes?

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What is the Dentinogenesis Imperfecta Treatment?

Construction of jacket crown for anterior teeth.
Construction of metal crown for posterior teeth.

What are the Dentinogenesis Imperfecta Symptoms and Signs?

The enamel appears normal but uniformly brownish or purplish and abnormally translucent. The form of the teeth is essentially normal, but the crowns of the molars tend to be bulbous and the roots are usually short. Enamel is weakly attached and tends to chip away from the dentine abnormally easily. In severe cases, the teeth become rapidly worn down to the gingivae. Early ﬁtting of full dentures then becomes inevitable as the relatively soft dentine and short roots make crowning impractical. In some patients, only a few teeth are severely affected, while the remainder appears normal. Radiographically, the main features are obliterated pulp chambers and stunted roots.